Abdominal pain in a patient with sickle cell disease with multiple complications/Coklu komplikasyonlarla birlikte orak hucre hastaligi olan bir hastada karin agrisi.

Sickle cell disease is an inherited autosomal recessive hemoglobinopathy. Acute abdominal pain is the cause of hospitalization in 10% of patients with sickle cell disease and usually occurs during vaso-occlusion or distal tissue ischemia. Determining the etiology of abdominal pain is very difficult in these patients because it is associated with several rare diagnoses, such as pancreatitis and splenic abscess in some patients. We represent a 14-year-old boy with sickle cell disease who was hospitalized due to acute abdominal pain and indicated multiple and scarce disturbances in the spleen and hepatobiliary system. Keywords: Abdominal pain; cholelithiasis; pancreatitis; sickle cell disease; splenic abscess Orak hucre hastaligi, otozomal resesif kalitim gecisli bir hemoglobinopatidir. Orak hucre hastaligi olan hastalarin %10'unda hastaneye yatis nedeni akut karin agrisidir ve bu durum genellikle vazo-okluzif tikanma ya da enfarktif kriz, distal doku iskemisi esnasinda ortaya cikar. Bu hastalarda, karin agrisinin etiyolojisinin tanisi cok zordur, Cunku bazi hastalarda pankreatit ve dalak absesi gibi bazi nadir durumlarla iliskili olabilir. Burada, akut karin agrisi nedeni ile yatirilan, orak hucre hastaligi olan ve dalak ve hepatobiliyer sistemde nadir gorulen coklu bozukluklar gosteren 14 yasinda bir erkek cocugunu sunuyoruz. Anahtar sozcukler: Dalak absesi; karin agrisi; kolelitiazis; orak hucre hastaligi; pankreatitis